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Small bowel T-cell lymphoma: a MEITL-ing diagnosis

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Abstract

Monomorphic epitheliotropic intestinal T-cell lymphoma (MEITL), previously known as Type-II enteropathy-associated T-cell lymphoma (EATL), is a rare subset of relatively aggressive lymphoma with a poor prognosis. We present a case of a previously healthy 59-year-old male with a 2-week history of abdominal distention who was found to have a non-bleeding ulcerated segment in the proximal jejunum secondary to MEITL. This exceedingly rare type of lymphoma usually presents with non-specific symptoms and can be challenging to diagnose. Our case demonstrates the importance of understanding the endoscopic and histological findings to allow the prompt diagnosis and treatment of this aggressive disease.

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Authors and Affiliations

  1. Department of Medicine, University of Connecticut Health Center, Farmington, CT, USA

    Sheena Mago

  2. Department of Medicine, Division of Gastroenterology-Hepatology, University of Connecticut Health Center, Farmington, CT, USA

    Marianna Mavilia & Haleh Vaziri

  3. Department of Pathology and Laboratory Medicine, University of Connecticut Health Center, Farmington, CT, USA

    Faripour Forouhar

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  1. Sheena Mago
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  2. Marianna Mavilia
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  3. Faripour Forouhar
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Correspondence to Haleh Vaziri.

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Sheena Mago, Marianna Mavilia, Faripour Forouhar, and Haleh Vaziri declare that they have no conflict of interest.

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Mago, S., Mavilia, M., Forouhar, F. et al. Small bowel T-cell lymphoma: a MEITL-ing diagnosis. Clin J Gastroenterol 14, 1071–1083 (2021). https://doi.org/10.1007/s12328-021-01417-3

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  • DOI: https://doi.org/10.1007/s12328-021-01417-3

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