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Enteropathy-Associated T Cell Lymphoma Presenting with Acute Abdominal Syndrome: a Case Report and Review of Literature

  • Case Report
  • Published:
Journal of Gastrointestinal Surgery

Abstract

Introduction

Enteropathy-associated T cell lymphoma (EATL) is a rare peripheral non-Hodgkin's T cell lymphoma originating from intraepithelial T lymphocytes of the intestines. In general, this condition has a poor prognosis. A common initial presentation of this cancer which is a small intestinal perforation necessitating emergency surgery is of interest to practicing surgeons. The diagnosis is rarely made prior to pathological examination.

Methods

We report a case of a 39-year-old African American man who presented with acute abdomen and was found to have a deep necrotic ulcer of the jejunum during exploratory laparotomy.

Results

Pathological examination and laboratory results demonstrated EATL, type 2, which is not associated with celiac disease. A review of the literature on EATL is also presented.

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Authors and Affiliations

  1. Department of Surgery, University of California, Davis Medical Center, Sacramento, USA

    Yifan Yang & Ho Phan

  2. Department of Pathology, University of California, Davis Medical Center, Sacramento, USA

    Mingyi Chen & Dariusz Borys

  3. University of California, Davis Medical School, Sacramento, USA

    Sukhjeet S. Batth

Authors
  1. Yifan Yang
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  2. Sukhjeet S. Batth
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  3. Mingyi Chen
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  4. Dariusz Borys
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  5. Ho Phan
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Correspondence to Yifan Yang.

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Yang, Y., Batth, S.S., Chen, M. et al. Enteropathy-Associated T Cell Lymphoma Presenting with Acute Abdominal Syndrome: a Case Report and Review of Literature. J Gastrointest Surg 16, 1446–1449 (2012). https://doi.org/10.1007/s11605-012-1878-6

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  • DOI: https://doi.org/10.1007/s11605-012-1878-6

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