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Pleuropulmonary blastoma—a case report and review of literature

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Pleuropulmonary blastoma (PPB) is a very rare, highly aggressive and malignant tumour originating from either the lungs or pleura. It occurs mainly in children of less than 5 or 6 years but may occur in adults rarely. It has a poor prognosis with three different subtypes: cystic (type I), combined cystic and solid (type II) and solid (type III). The PPB should be treated aggressively with surgery and chemotherapy. Here, we report a case of a 14-year-old boy presenting with acute respiratory distress because of left-side PPB. He underwent left-side thoracotomy with surgical resection of PPB followed by adjuvant chemotherapy.

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Authors and Affiliations

  1. Department of CVTS, Fifth floor, Grant Medical College, Byculla, Mumbai, Pin-400008, Maharashtra, India

    Suraj Wasudeo Nagre, Krishnarao Narayanrao Bhosle, Asif Shaikh & Vignesh Ravikumar

Authors
  1. Suraj Wasudeo Nagre
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  2. Krishnarao Narayanrao Bhosle
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  3. Asif Shaikh
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  4. Vignesh Ravikumar
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Correspondence to Suraj Wasudeo Nagre.

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No funding was required for this study.

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The authors declare that they have no conflict of interest.

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All procedures performed in studies involving human participants were in accordance with the ethical standards of the institution and national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

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Nagre, S.W., Bhosle, K.N., Shaikh, A. et al. Pleuropulmonary blastoma—a case report and review of literature. Indian J Thorac Cardiovasc Surg 34 (Suppl 1), 72–75 (2018). https://doi.org/10.1007/s12055-017-0574-2

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  • DOI: https://doi.org/10.1007/s12055-017-0574-2

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