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Pleuropulmonary Blastoma

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Soft Tissue Tumors

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Abstract

Pleuropulmonary blastoma is a malignant mesenchymal tumor of the thorax. Its cell origin is uncertain (probably a mesenchymal stem cell).

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Notes

  1. 1.

    MSA: muscle-specific actin.

  2. 2.

    EMA: epithelial membrane antigen.

  3. 3.

    GFAP: glial fibrillary acidic protein.

  4. 4.

    NSE: neuron-specific enolase.

  5. 5.

    TTF1: thyroid transcription factor 1 (also known as NKX2–1, NK2 homeobox 1); it encodes a protein expressed in thyroid as well as lung carcinoma.

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Authors and Affiliations

  1. Department of Surgery Oncology and Gastroenterology, University of Padova, Padova, Italy

    Simone Mocellin

  2. Melanoma and Soft Tissue Sarcoma Unit, Istituto Oncologico Veneto (IOV-IRCCS) of Padova, Padova, Italy

    Simone Mocellin

Authors
  1. Simone Mocellin
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Correspondence to Simone Mocellin .

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Mocellin, S. (2021). Pleuropulmonary Blastoma. In: Soft Tissue Tumors . Springer, Cham. https://doi.org/10.1007/978-3-030-58710-9_208

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  • DOI: https://doi.org/10.1007/978-3-030-58710-9_208

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-58709-3

  • Online ISBN: 978-3-030-58710-9

  • eBook Packages: MedicineMedicine (R0)

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