The authors described a 52-year-old male with a large right coronary sinus of Valsalva successfully treated by the Bentall operation. Although the patient had no typical sings of Marfan syndrome, the histological examination showed elastic fiber lacking and mucin deposits in the media which resembles the findings of cystic medial necrosis. Choice of surgical procedure seems to be appropriate because if aortic sinus replacement was selected, remaining tissue may cause later events such as aneurysmal change or dissection since histological changes might have occurred in the other part of the aorta. And also long-term results of the Bentall operation are satisfactory with a little complication rate [1, 2]. However, the Bentall operation using a mechanical valve needs lifetime anticoagulation therapy and it is a burden for the patient.

In 1995, David [3] introduced the various surgical techniques of aortic sparing operation in patients with aortic insufficiency and aortic root aneurysm. In the report, sinus replacement was described as a type of remodeling operation.

We have been treated two cases of aneurysm of right sinus of Valsalva with moderate aortic regurgitation. One patient had sinus replacement and aortic valve repair; however, this patient needed a reoperation, aortic valve replacement using a mechanical valve, 5 years after the initial operation due to exacerbation of AR. Another patient with Marfan syndrome underwent reimplantation procedure with use of a 24-mm polyester graft with pseudosinuses [4]. The patient was a 55-year-old female having a 5 × 5 cm aneurysm of the right sinus of Valsalva and has been doing well without aortic regurgitation.

In terms of the results of surgery for Marfan syndrome, Patel et al. [5] reported 140 patients in which 56 patients had composite grafts and 84 received valve-sparing operations. There were no hospital deaths in the both group and the patient survival rate at 8 years was 100 % for the valve-sparing group and 90.1 % for the composite graft group. In the series by David [6], of 103 patients (26 remodeling and 77 reimplantation technique), there was 1 hospital death and the patient survival rate at 15 years was 87.2 %. The aortic valve-sparing operations bring satisfactory results to the patients with Marfan syndrome.

Although the authors applied the Bentall procedure for the patient, valve-sparing operations are another useful option that we have to consider.