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Ewing’s sarcoma of the urogenital tract

  • Urology - Review
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Abstract

This article reviews the current available information on Ewing’s sarcoma of the urogenital tract, focusing on the presentation, diagnosis, and therapeutic management of this uncommon entity. Because of the rapid local growth of these tumors, an immediate decision for treatment initiation is mandatory. The classical presentation depends mainly on the site of involvement of these tumors, involving a palpable mass, hematuria, and pain. No specific diagnostic imaging is available to date, and the only diagnostic method remains histological examination in combination with immunohistochemistry. Treatment involves primary surgical resection of all tumor tissues followed by adjuvant multi-agent chemotherapy. Overall survival is poor, although a 13-year survival has been reached in one case.

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Authors and Affiliations

  1. Department of Urology and Paediatric Urology, Schleswig Holstein, Campus Kiel, Arnold Heller Str. 7, 24105, Kiel, Germany

    Amr Al-Najar, Carsten Maik Naumann, Moritz Franz Hamann, Peter-Klaus Jünemann & Christof van der Horst

  2. Department of Heart and Vascular Surgery, Schleswig Holstein, Campus Kiel, Kiel, Germany

    Markus Siggelkow

Authors
  1. Amr Al-Najar
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  2. Markus Siggelkow
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  3. Carsten Maik Naumann
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  4. Moritz Franz Hamann
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  5. Peter-Klaus Jünemann
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  6. Christof van der Horst
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Corresponding author

Correspondence to Amr Al-Najar.

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Al-Najar, A., Siggelkow, M., Naumann, C.M. et al. Ewing’s sarcoma of the urogenital tract. Int Urol Nephrol 41, 13–17 (2009). https://doi.org/10.1007/s11255-008-9415-y

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  • DOI: https://doi.org/10.1007/s11255-008-9415-y

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