Atypically presenting kaposiform hemangioendothelioma of the knee: ultrasound findings

  • Iclal Erdem Toslak
  • Matthew Stegman
  • Michael P. Reiter
  • Güliz A. Barkan
  • Dariusz Borys
  • Jennifer E. Lim-Dunham
Case Report


Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor of early childhood and infancy. Kasabach–Merritt phenomenon, a common complication of KHE, is characterized by life-threatening thrombocytopenia, hemolytic anemia, and consumption coagulopathy. There may be atypical cases that do not present with Kasabach–Merritt phenomenon and do have atypical imaging findings. Knowledge of atypical imaging features may assist radiologists in identifying KHE. In this report, we present a 4-year-old case of KHE with atypical ultrasound findings.


Kaposiform hemangioendothelioma Ultrasonography Color Doppler imaging Soft-tissue mass Vascular tumor 


Compliance with ethical standards

Ethical statement

All procedures performed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Conflict of interest

All authors state that they have no conflicts of interest to declare.




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Copyright information

© The Japan Society of Ultrasonics in Medicine 2018

Authors and Affiliations

  1. 1.Department of RadiologyLoyola University Medical CenterMaywoodUSA
  2. 2.Loyola University Chicago Stritch School of MedicineMaywoodUSA
  3. 3.Department of PathologyLoyola University Medical CenterMaywoodUSA
  4. 4.Loyola University Medical Center and Chicago Stritch School of MedicineMaywoodUSA

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