Abstract
Two different anesthetic methods were employed for a patient with recessive dystrophic epidermolysis bullosa (R-DEB).
One was plexus brachial block in combination with ketamine infusion. The other was general anesthesia with N2O-O2-halothane via a face mask. In the former, no particular problem developed. In the later, however, some blisters were newly formed on the region where the anesthesist’s fingers were attached to hold a face mask.
Although mask anesthesia was considered to be not always suitable for patients with DEB, we chose it because tracheal intubation may cause more serious damage to the upper airway leading to airway obstruction.
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References
Fox T.: Notes on unusual or rare forms of skin disease IV. Congenital ulceration of the skin (two cases) with pemphigus eruption and arrest of development generally. Lancet 766–7, 1879
Pearson RW.: The mechanobullous diseases (epidermolysis bullosa) In: Fitzpatrick TB, ed. Dermatology in general medicine. New York; McGraw Hill 621–43, 1971
Pearson RW, Spargo B.: Electron microscopic studies of dermal-epidermal separation in human skin. J Invest Dermatol 36:213–224, 1961
Pearson RW.: Studies on the pathogenesis of epidermolysis bullosa. J Invest Dermatol 39:551–575, 1962
Wright JT, Birmingham MS, Ala: Epidermolysis bullosa: dental and anesthetic management of two cases. Oral Surgery 27:155–157, 1984
Kelly RE, Koff RD, Rothaus KO.: Brachial plexus anesthesia in eight patients with recessive dystrophic epidermolysis bullosa. Anesth Analg 66:1318–20, 1987
Iovall J.: Ketamine monoanaesthesia for major surgery in epidermolysis bullosa, Case report. Acta Anaesthesiol Scand 31:658–660, 1987
Mahshall BE: A comment on epidermolysis bullosa and its anaesthetic management for dental operations. Br J Anaeth. 35:724–727, 1963
Dundee W, Riding JE.: Barbiturate narcosis in porphyria. Anaesthesia 10,55–58, 1955
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Tsukamoto, N., Kobayashi, E., Kasuda, H. et al. Anesthesia for a patient with recessive dystrophic epidermolysis bullosa. J Anesth 3, 223–226 (1989). https://doi.org/10.1007/s0054090030223
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DOI: https://doi.org/10.1007/s0054090030223