Abstract
Malignant rhabdoid tumor (MRT) is a recently described variety of childhood renal neoplasm. MRT arising primarily in the central nervous system (CNS) is still a rather unfamiliar pathological entity and is frequently misdiagnosed as medulloblastoma or primitive neuroectodermal tumor (PNET). We describe a 7-month-old boy who harbored a CNS-MRT that originated within the IV ventricle and invaded the brain stem and the cerebellar hemispheres. After an initial documented good response to chemotherapy the tumor recurred locally 9 months after operation. We discuss clinical and histopathological features distinguishing between PNET/medulloblastoma and MRTs. Current literature on MRT of the CNS is briefly reviewed.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Received: 17 October 1996
Rights and permissions
About this article
Cite this article
Martínez-Lage, J., Nieto, A., Sola, J. et al. Primary malignant rhabdoid tumor of the cerebellum. Child's Nerv Syst 13, 418–421 (1997). https://doi.org/10.1007/s003810050112
Issue Date:
DOI: https://doi.org/10.1007/s003810050112