Abstract
Cerebral proliferative angiopathies (CPAs) are distinct vascular malformations with varied clinical presentations and radiological findings from arteriovenous malformations (AVM) (Lasjaunias et al. in Stroke 39(3):878–85, 2008). They usually manifest with seizures if present supratentorial, headache, and progressive neurological deficits due to steal phenomenon or rarely with hemorrhage (Lasjaunias et al. in Stroke 39(3):878–85, 2008). Most of the patients are usually young females. Pediatric cases are extremely rare, with few cases reported till now. Here we report a child who presented with cerebellar bleed and diagnosed as CPA. The child was managed medically, and there was no change in caliber of the vessels after 18 months of follow-up. A short review of cases of CPA in pediatric age group presentations and management was undertaken in this case report.
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Beniwal, M., Kandregula, S., Aravind et al. Pediatric cerebral proliferative angiopathy presenting infratentorial hemorrhage. Childs Nerv Syst 36, 429–433 (2020). https://doi.org/10.1007/s00381-019-04313-x
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DOI: https://doi.org/10.1007/s00381-019-04313-x