Abstract
We report a rare cause of cervical myelopathy (CM) in a 10-year-old Down syndrome (DS) girl. She presented with progressive CM over 1 year affecting her ability to ambulate or feed herself. The myelopathy was secondary to C2/3 instability. Surgical reduction and instrumented fusion have significantly improved her neurological status. This case emphasizes the importance of close follow-up of DS patients for early diagnosis and treatment of cervical spine abnormalities.
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Al-Habib, A., AlAqeel, A. C2/3 instability: unusual cause of cervical myelopathy in a child with Down syndrome. Childs Nerv Syst 29, 163–165 (2013). https://doi.org/10.1007/s00381-012-1950-2
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DOI: https://doi.org/10.1007/s00381-012-1950-2