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A rare adult case of asymptomatic double aortic arch accompanied by the right vertebral artery directly originating from the aortic arch

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Abstract

Introduction

A double aortic arch (DAA) is a rare congenital vascular anomaly. No case of DAA with a direct aortic origin of the right vertebral artery (VA) has been reported in adults. Here, we report a rare case of an asymptomatic DAA accompanied by the right VA directly originating from the right aortic arch in an adult.

Case presentation

A DAA and right VA directly originating from the right aortic arch were identified in a 63-year-old man using digital subtraction angiography and computed tomography angiography. The patient underwent digital subtraction angiography for evaluation of an unruptured cerebral aneurysm. Intraprocedural selection of vessels branching from the aorta with the catheter was difficult. To confirm the bifurcation of the aorta, aortography was performed, which revealed a DAA. Following digital subtraction angiography, computed tomography angiography was performed, which showed that the right VA originated directly from the right aortic arch. The trachea and esophagus were located in the vascular ring of the DAA; however, they were not compressed by the aorta. This was consistent with the lack of symptoms related to the DAA.

Conclusions

This is the first adult case of an asymptomatic DAA with an unusual origin of the VA. A rare asymptomatic vascular anomaly, such as a DAA, can be incidentally identified using angiography.

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Availability of data and materials

The data sets generated and/or analyzed during the current study are available from the corresponding author on reasonable request.

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Authors

Contributions

MA data collection, figure drawing, manuscript writing, and project development. YM manuscript writing. MH manuscript revising. TH final approval of this study.

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Correspondence to Mitsushige Ando.

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The authors have no relevant financial or non-financial interests to disclose.

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This study complied with all the relevant national regulations and institutional policies and was performed in accordance the tenets of the Declaration of Helsinki. This study was approved by the authors’ institutional review board or equivalent committee.

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We obtained written informed consent from the patient.

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Ando, M., Maki, Y., Hojo, M. et al. A rare adult case of asymptomatic double aortic arch accompanied by the right vertebral artery directly originating from the aortic arch. Surg Radiol Anat 45, 637–641 (2023). https://doi.org/10.1007/s00276-023-03120-z

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