Abdominal Radiology

, Volume 43, Issue 2, pp 285–300 | Cite as

Rare pancreatic tumors

  • Jonathan Steinman
  • Atif Zaheer
  • Michael D. Kluger
  • Helen Remotti
  • Elizabeth M. HechtEmail author


In this review, we will focus on rare pancreatic tumors. Most of these tumors do not have distinct characteristic appearances so the key to diagnosis requires a combination of imaging appearance, laboratory data, patient demographics, and associated medical syndromes in order to narrow the differential diagnosis. Nonetheless, imaging plays a vital role in narrowing the differential and guiding management. While there are many variant pathologic entities that cannot be encompassed by a single review, we aim to illustrate the imaging appearance of less common pancreatic tumors highlighting key distinctive diagnostic characteristics and discuss the implications for management. While there is overlap in the imaging appearances of many of these entities, for educational purposes, lesions will be categorized into solid (hypoenhancing and hyperenhancing), cystic lesions, mesenchymal neoplasms, and neoplasms seen in younger patients (< 40 years).


Pancreas Pancreas cancer Pancreatic ductal adenocarcinoma Acinar tumors MRI CT 


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Copyright information

© Springer Science+Business Media, LLC 2017

Authors and Affiliations

  • Jonathan Steinman
    • 1
  • Atif Zaheer
    • 2
  • Michael D. Kluger
    • 3
  • Helen Remotti
    • 4
  • Elizabeth M. Hecht
    • 1
    Email author
  1. 1.Columbia University Medical CenterNew YorkUSA
  2. 2.Johns Hopkins University School of MedicineBaltimoreUSA
  3. 3.Columbia University Medical CenterNew YorkUSA
  4. 4.Columbia University Medical CenterNew YorkUSA

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