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Pancreatitis, panniculitis, and polyarthritis (PPP) syndrome: MRI features of intraosseous fat necrosis involving the feet and knees

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Abstract

Pancreatitis, panniculitis, and polyarthritis (PPP) syndrome is extremely rare and presents as a triad of the three diseases. The patient usually presents with mild or absent abdominal symptoms. Here, we report on a case of a 66-year-old male who presented with pain and swelling in both legs and mild abdominal pain. He was diagnosed with acute pancreatitis by pancreatic enzyme analysis and abdominal computed tomography (CT) and with skin lesions of panniculitis through a biopsy. Magnetic resonance imaging (MRI) revealed multifocal intraosseous fat necrosis and arthritis involving both the feet and the knees. Therefore, we report a case of PPP syndrome with intraosseous fat necrosis involving both the feet and the knees.

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Authors and Affiliations

  1. Department of Radiology, Inje University College of Medicine, Busan Paik Hospital, 75 Bokjiro, Busanjin-gu, Busan, 614-735, South Korea

    Dong Joo Kang, Sun Joo Lee & Hye Jung Choo

  2. Division of Rheumatology, Department of Internal Medicine, Inje University College of Medicine, Busan Paik Hospital, Busan, South Korea

    Minyoung Her

  3. Department of Pathology, Inje University College of Medicine, Busan Paik Hospital, Busan, South Korea

    Hye Kyoung Yoon

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  1. Dong Joo Kang
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  2. Sun Joo Lee
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  3. Hye Jung Choo
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  4. Minyoung Her
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Correspondence to Sun Joo Lee.

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Kang, D.J., Lee, S.J., Choo, H.J. et al. Pancreatitis, panniculitis, and polyarthritis (PPP) syndrome: MRI features of intraosseous fat necrosis involving the feet and knees. Skeletal Radiol 46, 279–285 (2017). https://doi.org/10.1007/s00256-016-2549-6

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  • DOI: https://doi.org/10.1007/s00256-016-2549-6

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