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Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy

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Abstract

Epithelioid hemangioendothelioma of the liver is a very rare vascular tumour in children with intermediate malignant potential. We present a case in which the typical imaging appearances of coalescent peripheral hepatic masses with capsular retraction contributed to the diagnosis. A positron emission tomography-CT (PET-CT) procedure was performed in staging the disease with a strong suspicion of coeliac nodal involvement confirmed after laparotomy and histological analysis. Our case is unique because of the rarity of the disease, the young age of the child, and proven nodal metastases at initial diagnosis. The use of PET-CT allows better staging at initial diagnosis and thus better management with improved follow-up in these patients.

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Authors and Affiliations

  1. Service de Radiologie et Imagerie Médicale, Hôtel Dieu, CHU Clermont-Ferrand, Bd Léon Malfreyt, Clermont-Ferrand, 63058, France

    David Da Ines, Virginie Petitcolin & Jean-Marc Garcier

  2. Service d’Anatomopathologie, Hôtel Dieu, CHU Clermont-Ferrand, Clermont-Ferrand, France

    Juliette Joubert-Zakeyh

  3. Service de Pédiatrie Générale et Multidisciplinaire, Hôtel Dieu, CHU Clermont-Ferrand, Clermont-Ferrand, France

    Francois Demeocq

Authors
  1. David Da Ines
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  2. Virginie Petitcolin
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  3. Juliette Joubert-Zakeyh
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  4. Francois Demeocq
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  5. Jean-Marc Garcier
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Correspondence to David Da Ines.

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Da Ines, D., Petitcolin, V., Joubert-Zakeyh, J. et al. Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy. Pediatr Radiol 40, 1293–1296 (2010). https://doi.org/10.1007/s00247-009-1532-y

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  • DOI: https://doi.org/10.1007/s00247-009-1532-y

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