Abstract
Hepatic epithelioid haemangioendothelioma (HEHE) is extremely rare in children. We present an adolescent who presented with a scoliosis due to left thoracic pain. Multifocal HEHE was incidentally found during CT scan of the thorax, and confirmed with a multiphase CT scan of the abdomen, biopsy and immunochemistry. Left pleural and pulmonary involvement was suspected and later confirmed with biopsy and histopathological examination. The patient died 1 year after diagnosis. To the best of our knowledge, scoliosis has not previously been reported as the first symptom of EHE.
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Caruso, S., Miraglia, R., Maruzzelli, L. et al. An unusual presentation of malignant hepatic epithelioid haemangioendothelioma with left pleural and pulmonary localization. Pediatr Radiol 38, 1027–1030 (2008). https://doi.org/10.1007/s00247-008-0915-9
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DOI: https://doi.org/10.1007/s00247-008-0915-9