Abstract
We report a young woman with primary cerebral non-Langerhans cell histiocytosis of the juvenile xanthogranuloma family. The clinical course was complicated by extensive infiltration of cranial nerves and meninges and epi- and intramedullary spinal dissemination. Whereas the cutaneous form of juvenile xanthogranuloma is usually benign and self-limited, central nervous system involvement is associated with high morbidity and mortality and might therefore be considered a separate clinical entity.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Electronic Publication
Rights and permissions
About this article
Cite this article
Ernemann, U., Skalej, M., Hermisson, M. et al. Primary cerebral non-Langerhans cell histiocytosis: MRI and differential diagnosis. Neuroradiology 44, 759–763 (2002). https://doi.org/10.1007/s00234-002-0819-6
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00234-002-0819-6