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Bullöser systemischer Lupus erythematodes

Bullous systemic lupus erythematosus

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Zusammenfassung

Der bullöse systemische Lupus erythematodes ist eine seltene Erkrankung, die mit subepidermaler Blasenbildung einhergeht und meistens mit schwerer systemischer Manifestation assoziiert ist. Wir berichten über einen 19-jährigen Patienten mit einem systemischen Lupus erythematodes, der im Verlauf seiner Erkrankung bullöse Hautveränderungen unter gleichzeitiger Verschlechterung des Allgemeinbefindens entwickelte, und diskutieren die verschiedenen Varianten von bullösen Hautveränderungen, die im Rahmen eines Lupus erythematodes auftreten können.

Abstract

Bullous systemic lupus erythematosus is a rare disease associated with subepidermal blistering and, in most cases, severe systemic manifestations. We describe a 19-year-old man with systemic lupus erythematosus who developed a bullous eruption along with a flare-up of systemic manifestations during the course of his disease and discuss the different forms of bullous lesions in patients with lupus erythematosus.

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Authors and Affiliations

  1. Hautklinik, Universitätsklinikum Düsseldorf, Düsseldorf

    D. Bacman, M. Megahed, T. Ruzicka &  A. Kuhn

  2. Klinik für Nephrologie und Rheumatologie, Universitätsklinikum Düsseldorf, Düsseldorf

    B. Ostendorf & M. Schneider

  3. Hautklinik, Universitätsklinikum Düsseldorf, Moorenstraße 5, 40225 , Düsseldorf

    A. Kuhn

Authors
  1. D. Bacman
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  2. B. Ostendorf
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  3. M. Megahed
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  4. T. Ruzicka
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  5. M. Schneider
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  6. A. Kuhn
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Corresponding author

Correspondence to A. Kuhn.

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Bacman, D., Ostendorf, B., Megahed, M. et al. Bullöser systemischer Lupus erythematodes. Hautarzt 55, 392–395 (2004). https://doi.org/10.1007/s00105-004-0715-6

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  • DOI: https://doi.org/10.1007/s00105-004-0715-6

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