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Juvenile colonic polyposis with villous adenoma and retroperitoneal fibrosis: Report of a case

  • Published:
Diseases of the Colon & Rectum

Summary

A 25-year-old Nigerian black woman was found to have polyps involving the rectum, rectosigmoid, and sigmoid colon on air-contrast barium-enema examination. Resection of a segment of sigmoid colon revealed numerous polyps that were predominantly of the juvenile type, in keeping with the diagnosis of juvenile polyposis of the colon. This case is unusual because of the coexistence of retroperitoneal fibrosis with juvenile polyposis of the colon. In addition, one of the colonic polyps was a villous adenoma. The implications of these findings are discussed in relation to polyposis syndromes reported previously.

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Authors and Affiliations

  1. Department of Pathology, Huron Road Hospital, 13951 Terrace Road, 44112, Cleveland, Ohio

    Erwin R. Rabin M.D., Tarulata Patel M.D., Fong-Hsiung Chen M.D., Sahap Gunalp M.D. & Henry W. Brown M.D.

  2. Departments of Surgery, Huron Road Hospital, Cleveland, Ohio

    Erwin R. Rabin M.D., Tarulata Patel M.D., Fong-Hsiung Chen M.D., Sahap Gunalp M.D. & Henry W. Brown M.D.

Authors
  1. Erwin R. Rabin M.D.
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  2. Tarulata Patel M.D.
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  3. Fong-Hsiung Chen M.D.
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  4. Sahap Gunalp M.D.
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  5. Henry W. Brown M.D.
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Rabin, E.R., Patel, T., Chen, FH. et al. Juvenile colonic polyposis with villous adenoma and retroperitoneal fibrosis: Report of a case. Dis Colon Rectum 22, 63–67 (1979). https://doi.org/10.1007/BF02586762

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  • DOI: https://doi.org/10.1007/BF02586762

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