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European Journal of Pediatrics

, Volume 155, Issue 10, pp 890–894 | Cite as

Complications of childhood Sjögren syndrome

  • I. Kobayashi
  • H. Furuta
  • A. Tame
  • N. Kawamura
  • K. Kojima
  • M. Endoh
  • M. Okano
  • Y. Sakiyama
Immunology/Allergology

Abstract

Sjögren syndrome (SS) is a common disorder in adults and involves both glandular and extraglandular systems. We report here four cases of childhood SS complicated by chronic thyroiditis, interstitial nephritis or sweat gland inflammation. Additionally, in one of these cases, the central nervous system was involved. All of these complications are common in adult cases.

Key words

Sjögren syndrome Renal tubular acidosis Interstitial nephritis Central nervous system disorder Chronic thyroiditis 

Abbreviations

dRTA

distal renal tubular acidosis

KCS

keratoconjunctivitis sicca

PSP

phenolsulphophthalein

s-GPT

serum glucose pyruvate transaminase

s-GOT

serum glutamate oxalate transaminase

SS

Sjögren syndrome

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Copyright information

© Springer-Verlag 1996

Authors and Affiliations

  • I. Kobayashi
    • 1
  • H. Furuta
    • 1
  • A. Tame
    • 1
  • N. Kawamura
    • 1
  • K. Kojima
    • 2
  • M. Endoh
    • 2
  • M. Okano
    • 1
  • Y. Sakiyama
    • 1
  1. 1.Department of PaediatricsHokkaido University School of MedicineKita-ku, SapporoJapan
  2. 2.Paediatric ClinicGoryokaku HospitalGoryokaku, HakodateJapan

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