Summary
Progressive diaphyseal dysplasia is a rare osteosclerotic dysplasia of the bone which presents clinically with bone pain, muscle weakness and a waddling gait. Radiography, which shows progressive hyperostosis along the long bones forms the basis of the diagnosis. We present a young patient in whom pain and limitation of movement in the shoulder joint area, mimicking capsulitis, were the presenting symptoms of the disease. The diagnostic and the therapeutic approach to this unusual disorder are discussed.
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Schapira, D., Militeanu, D., Israel, O. et al. Progressive diaphyseal dysplasia masquerading as shoulder capsulitis in an adult. Clin Rheumatol 14, 582–585 (1995). https://doi.org/10.1007/BF02208162
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DOI: https://doi.org/10.1007/BF02208162