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Malignant potential of juvenile polyposis coli

Report of a case and review of the literature

  • Case Reports
  • Published:
Diseases of the Colon & Rectum

Abstract

Juvenile polyps of the colon and rectum traditionally have been viewed as being benign inflammatory or harmartomatous lesions without potential for malignant change. The authors report a case of adenocarcinoma developing in a patient with sporadic juvenile polyposis. Juvenile polyposis was diagnosed in the patient at age 4 years. He underwent subtotal colectomy at age 6 years. At age 12, he underwent a proctectomy and a Swenson pull-through because of adenomatous changes in the rectal stump. At age 19 surveillance endoscopy revealed invasive cancer in a juvenile polyp.

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Authors and Affiliations

  1. Department of Surgery, Sections of Pediatric Surgery and Surgical Pathology, Yale New Haven Hospital, Yale University School of Medicine, New Haven, Connecticut

    Walter E. Longo M.D., Robert J. Touloukian M.D., A. Brian West M.D. & Garth H. Ballantyne M.D.

Authors
  1. Walter E. Longo M.D.
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  2. Robert J. Touloukian M.D.
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  3. A. Brian West M.D.
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  4. Garth H. Ballantyne M.D.
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Additional information

Read at the Spring Meeting of the New England Society of Colon and Rectal Surgeons, Newport, Rhode Island, April 15, 1989.

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Cite this article

Longo, W.E., Touloukian, R.J., West, A.B. et al. Malignant potential of juvenile polyposis coli. Dis Colon Rectum 33, 980–984 (1990). https://doi.org/10.1007/BF02139111

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  • DOI: https://doi.org/10.1007/BF02139111

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