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Congenital histiocytosis X

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Abstract

Congenital histiocytosis X involving multiple organs is a rare disease that causes rapid mortality in intrauterine and neonatal life. The diagnosis of histiocytosis X (Litterer-Siwe disease should be considered in a neonate with vesiculated crusting skin lesions. We present clinical, radiographic and histopathological findings in a neonate with congenital histiocytosis who died of respiratory failure due to diffuse infilteration of lungs with histiocytic cells.

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Authors and Affiliations

  1. Department of Radiology, Loyola University Medical Center, 2160 S. First Avenue, 60153, Maywood, Illinois, USA

    A. Vade & K. L. Pierce

  2. Department of Pediatrics, Loyola University Medical Center, Maywood, Illinois, USA

    A. Hayani

Authors
  1. A. Vade
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  2. A. Hayani
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  3. K. L. Pierce
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Vade, A., Hayani, A. & Pierce, K.L. Congenital histiocytosis X. Pediatr Radiol 23, 181–182 (1993). https://doi.org/10.1007/BF02013826

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  • DOI: https://doi.org/10.1007/BF02013826

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