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Intracerebral paraventricular hyperdensities: A new CT sign in Krabbe globoid cell leukodystrophy

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Journal of Inherited Metabolic Disease

Abstract

Computer-assisted tomographic (CT) scanning showed intracranial paraventricular calcification in two out of six patients with enzymatically and/or histologically confirmed Krabbe globoid cell leukodystrophy (GLD) 1–5 months after the onset of symptoms of the disease.

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Authors and Affiliations

  1. Departments of Pediatrics, Pathology and Radiology, Hospital for Sick Children, 555 University Avenue, M5G 1X8, Toronto, Ontario, Canada

    S. J. Feanny, S. H. Chuang, L. E. Becker & J. T. R. Clarke

Authors
  1. S. J. Feanny
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  2. S. H. Chuang
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  3. L. E. Becker
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  4. J. T. R. Clarke
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Feanny, S.J., Chuang, S.H., Becker, L.E. et al. Intracerebral paraventricular hyperdensities: A new CT sign in Krabbe globoid cell leukodystrophy. J Inherit Metab Dis 10, 24–27 (1987). https://doi.org/10.1007/BF01799484

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  • DOI: https://doi.org/10.1007/BF01799484

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