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Biliary disease in metachromatic leukodystrophy

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Abstract

This paper illustrates the previously unreported sonographic changes in the biliary tract in metachromatic leukodystrophy (MLD). Gallbladder wall thickening due to sulfatide deposition, intraluminal globules of sulfatide or papillomatosis may cause symptoms referrable to the biliary tract in these patients. A series of patients whom, we have studied is briefly alluded to in order to bring to the attention of the radiologist MLD as a rare cause of biliary disease in children.

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Authors and Affiliations

  1. Department of Radiology, the Hospital for Sick Children, 555 University Avenue, M5G1X8, Toronto, Ontario, Canada

    Linda Heier, A. Daneman, Susan Craw & D. J. Martin

  2. Department of Pediatrics, the Hospital for Sick Children, M5G1X8, Toronto, Ontario, Canada

    J. Alexander Lowden

  3. Department of Pathology, the Hospital for Sick Children, M5G1X8, Toronto, Ontario, Canada

    E. Cutz

  4. University of Toronto, M5G1X8, Toronto, Ontario, Canada

    E. Cutz

Authors
  1. Linda Heier
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  2. A. Daneman
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  3. J. Alexander Lowden
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  4. E. Cutz
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  5. Susan Craw
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  6. D. J. Martin
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Heier, L., Daneman, A., Alexander Lowden, J. et al. Biliary disease in metachromatic leukodystrophy. Pediatr Radiol 13, 313–318 (1983). https://doi.org/10.1007/BF01625956

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  • DOI: https://doi.org/10.1007/BF01625956

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