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Staphylocidal defect of polymorphonuclear leukocytes in a patient with Leprechaunism

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Abstract

A patient with the features of Leprechaunism had a severe and constant defect of bactericidal activity of his phagocytes. We suggest this abnormality might be the basis of the well known recurrence of infections in this syndrome.

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Sacchi, F., Maggiore, G., Bianchi, E. et al. Staphylocidal defect of polymorphonuclear leukocytes in a patient with Leprechaunism. Eur J Pediatr 137, 89–90 (1981). https://doi.org/10.1007/BF00441177

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  • DOI: https://doi.org/10.1007/BF00441177

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