Abstract
Familial ectodermal dysplasia in a tropical area is reported. All males in the third generation were suffering from partial anodontia and hypotrichosis. They also had saddle-shaped noses and protuberant lips. The youngest boy had all deciduous teeth missing, in addition to oligodontia of the permanent dentition and hypotrichosis congenita. The sisters had normal dentition and normal hair.
The parents and maternal grandmother also had normal hair, but their dentition, except that of the male parent, was reported not to be.
It is suggested that the ectodermal dysplasia may be a hereditary disorder with a recessive sex-linked mode of inheritance.
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Cove-Smith, R.: Congenital ectodermal defect. Proc. roy. Soc. Med. 23, 1407 (1929)
Everett, F. G., Jump, E. B., Sutherland, W. F., Savara, B. S., Suher, T.: Anhidrotic ectodermal dysplasia with anodontia. A study of two families. J. Amer. dent. Ass. 44, 173 (1952)
Guilford, S. H.: Dental anomaly. Dent. Cosmos. 25, 113 (1883)
Keeler, C. E.: Heredity in dentistry. Dent. Cosmos. 77, 1147 (1935)
Mahloudji, M., Livingston, K. E.: Familial and congenital simple anhidrosis. Amer. J. Dis. Childh. 113, 477 (1967)
Redpath, T. H., Winter, G. B.: Autosomal dominant ectodermal dysplasia with significant dental defects. Brit. dent. J. 126 123 (1969)
Thadani, K. I.: A toothless type of man. J. Hered. 12, 87 (1921)
Thoma, K. H., Allen, F. W.: Anodontia in ectodermal dysplasia. Amer. J. orthop. oral Surg. 26, 503 (1940)
Thoma, K. H., Goldman, H. M.: Oral pathology, ed. 5, St. Louis: Mosby 1960
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Yoshinaga, T., Miyoshi, S., Nishijima, S. et al. A case of familial ectodermal dysplasia. Z. Kinder-Heilk. 115, 77–82 (1973). https://doi.org/10.1007/BF00438993
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DOI: https://doi.org/10.1007/BF00438993