Summary
The cellular inflammatory response was studied by the “skin window” technique in 5 patients with “myogenic” scapuloperoneal syndrome, 15 cases of progressive muscular dystrophy, 10 cases of the Charcot-Marie-Tooth disease, 10 cases of amyotrophic lateral sclerosis, and in 15 patients after acute poliomyelitis. A comparison with 146 controls showed normal conditions in patients with muscular dystrophy, whereas in 4 patients with the scapuloperoneal syndrome, in patients with Charcot-Marie-Tooth disease, in cases of ALS, and in some patients after poliomyelitis, the migration of macrophages into the inflammatory field was delayed. The authors conclude that the pathogenesis of the “myogenic” scapuloperoneal syndrome differs from the pathogenesis of progressive muscular dystrophy by a participation of the neurogenic disorder.
Zusammenfassung
Die celluläre Entzündungsreaktion wurde mit Hilfe der „Hautfenster-Methode“ bei 5 Kranken mit einem „myogenen“ scapuloperonealen Syndrom, 15 Fällen progressiver Muskeldystrophie, 10 Fällen von Charcot-Marie-Toothscher Krankheit, 10 Fällen von amyotrophischer Lateralsklerose und bei 15 Patienten nach durchgemachter akuter Poliomyelitis untersucht. Ein Vergleich mit 146 Kontrollpersonen zeigte normale Verhältnisse bei den Kranken mit Muskeldystrophie, während bei 4 Kranken mit scapuloperonealem Syndrom, den Kranken mit Charcot-Marie-Toothscher Krankheit und mit ALS sowie in einigen postpoliomyelitischen Fällen die Migration von Makrophagen ins entzündliche Feld verzögert war. Die Autoren schlußfolgern, daß die Pathogenese des scapuloperonealen Syndroms sich von der Pathogenese der Muskeldystrophie durch die Beteiligung neurogener Störung unterscheidet.
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Urbánek, K., Jansa, P., Steidl, L. et al. The course of a model cutaneous inflammation in the scapuloperoneal syndrome and in systemic neuromuscular diseases. J. Neurol. 208, 139–146 (1974). https://doi.org/10.1007/BF00312510
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DOI: https://doi.org/10.1007/BF00312510