Summary
A case of Ullrich-Noonan syndrome with the typical marked webbed neck deformity is presented. The posterior approach is preferred for the correction of the webbed neck deformity. Bilaterally localized excess skin and the underlying fibrotic bands were excised in an elliptical shape. The webbed neck was corrected by a large classical z-plasty. After the transposition of z-plasty flaps, the final appearance of the neck was cosmetically satisfactory.
This is a preview of subscription content, log in via an institution to check access.
Similar content being viewed by others
References
Acartürk S (1986) Correction of webbed neck deformity in Turner's syndrome. Chir Plastica 8:159–164
Agris J, Dingman RO, Varon J (1983) Correction of webbed neck defects. Ann Plast Surg 11:299
Barr ML, Bertrom LF, Lindsay HA (1950) The morphology of the nerve cell nucleus, according to sex. Anat Rec 107:283
Cronin TD (1977) Deformities of the cervical region. In: Converse JM (ed) Reconstructive plastic surgery. Saunders, Philadelphia, 2nd ed, Vol 3
Ford CE, Jones KW, Polani PE, de Almeida VC, Briggs VH (1959) A sex-chromosome anomaly in a case of gonadal dysgenesis (Turner's syndrome). Lancet 1:711
Foucar HO (1984) Pterygium colli and allied conditions. Can Med Assoc J 59:251
Funke (1902) Pterygium colli. Dtsch 2. Chir 3:162
Kobylinski O (1883) Ueber eine flughautähnliche Austreitung am Halse. Arch Anthropol 14:343
La Ruffa H (1970) Cirugia de las membranes cervicales olares (pterygium colli). Boletines y Trabajos Sociedad Argentina de Cirujanos. 31:572
Levy EP, Poshayan H, Fraser FC (1970) XX and XY Turner phenotype in a family. Am J Dis Child 120:36
Menick FT, Furnas DW, Achauer BM (1984) Lateral cervical advancement flaps for the correction of webbed neck deformity. Plast Reconstr Surg 73:223
Nora JJ, Nora AH, Sinka AK (1974) The Ullrich-Noonan syndrome (Turner phenotype). Am J Dis Child 127:48
Nora JJ, Sinka AK (1974) Direct male to male transmission of the xx phenotype. Lancet 1:250
Polani PE, Hunter WF, Lennox B (1954) Chromosomal sex in Turner syndrome with coaretation of the aorta. Lancet 11:120
Polani PE, Lessof MH, Bishop PMF (1956) Color blindness in “ovarian agenesis” (Gonadal dysplasia). Lancet 11: 118
Schröder F (1958) Die operative Korrektur des Pterygium colli. Arch Klin Chir 289:634
Sharpey SEP (1941) A case of pterygonuchal infantilism. Lancet 11:559
Shearin JC, de Franzo AJ (1980) Butterfly correction of webbed neck deformity in Turner syndrome. Plast Reconstr Surg 66:129
Soughin MR, Jackson NPU (1953) Turner's syndrome in the male. Br Med J 2:371
Steiker DD, Mellman WJ, Bongiovanni AM, Eberlain WR, Le Boeuf G (1961) Turner's syndrome in the male. J Pediatr 58:321
Turner HH (1938) A syndrome of infantilism, congenital webbed neck, and cubitus valgus. Endocrinology 23: 566
Wilkins L, Fleischmann W (1954) Ovarian agenesis: pathology, associated clinical symptoms and bearing on theories of sex differentiation. J Clin Endocrinol 14:1270
Wilkins L, Grumbach MM, Van Wky JJ (1954) Chromosomal sex in ovarian agenesis. J Clin Endocrinol 14:1270
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Durak, N., Aytemiz, C. Correction of pterygium colli deformity in Ullrich-Noonan Syndrome. Eur J Plast Surg 12, 25–28 (1989). https://doi.org/10.1007/BF00226917
Issue Date:
DOI: https://doi.org/10.1007/BF00226917