Abstract
Rhabdoid tumour of the kidney is a rare paediatric neoplasm usually associated with a grave prognosis. We report a case of left renal rhabdoid tumour with involvement of the inferior vena cava (IVC) and right atrium in a 13-year-old girl. Left nephrectomy together with removal of the IVC and atrial extension was undertaken on cardiopulmonary bypass and hypothermia. She remained disease-free and in good health for 1 year, however, recent review has shown recurrence in the abdominal lymph nodes.
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References
Akyon MG, Arslan G (1981) Pulmonary embolism during surgery for a Wilms' tumour (nephroblastoma). Case report. Br J Anaesth 53: 903–905
Bracken RB, Sutow WW, Jaffe N, Ayala A, Guarda L (1982) Preoperative chemotherapy for Wilms' tumour. Urology 19: 55–60
Bray GL, Pendergrass TW, Schaller RT Jr, Kiviat N, Beckwith JB (1986) Preoperative chemotherapy in the treatment of Wilms' tumor diagnosed with the aid of fine-needle aspiration biopsy. Am J Pediatr Hematol Oncol 8: 75–78
Clayman RV, Sheldon CA, Gonzales R (1982) Wilms' tumour: an approach to vena caval intrusion. Prog Pediatr Surg 15: 285–305
Gibson JM, Hall-Craggs MA, Dicks-Mireaux C, Finn JP (1990) Intracardiac extension of Wilms' tumour: demonstration by magnetic resonance. Br J Radiol 63: 568–569
Haas JE, Palmer NF, Weinberg AG, Beckwith JB (1981) Ultrastructure of malignant rhabdoid tumor of the kidney. A distinctive renal tumor of children. Hum Pathol 12: 646–657
Hunt TM, Firmin RK, Johnstone MJS (1988) Management of a patient with Wilms' tumour extending into the right heart chambers: a case report and a review of other published reports. Br Heart J 60: 165–168
Kogan SJ, Marans H, Santorineau M, Schneider K, Reda E, Levitt SB (1986) Successful treatment of renal vein and vena caval extension of nephroblastoma by preoperative chemotherapy. J Urol 136: 312–317
Krane RJ, deVere White R, Davis Z, Sterling R, Dobnik DB, McCormick JR (1984). Removal of renal cell carcinoma extending into the right atrium using cardiopulmonary bypass, profound hypothermia and circulatory arrest. J Urol 131: 945–947
Luck SR, Deleon S, Shkolnik A, Morgan E, Labotka R (1982) Intracardiac Wilms' tumor: diagnosis and management. J Pediatr Surg 17: 551–554
Nakayama DK, Norkool P, DeLorimier AA, O'Neill JA, D'Angio GJ (1986) Wilms' tumor. A report of National Wilms' Tumor Study. Ann Surg 204: 693–697
Ritchey ML, Kelalis PP, Breslow N, Offord KP, Shochat SJ, D'Angio SJ (1988) Intracaval and atrial involvement with nephroblastoma: review of National Wilms' Tumor Study — 3. J Urol 140: 1113–1118
Schaller RT Jr, Schaller TF, Buschmann C, Kiviat N (1983) The usefulness of percutaneous fine needle aspiration biopsy in infants and children. J Pediatr Surg 18: 398–405
Slovis TL, Philippart AI, Cushing B, Das L, Perlmutter AD, Reed JO, Wilner HI, Kroovand RL, Farooki ZQ (1981) Evaluation of the inferior vena cava by sonography and venography in children with renal and hepatic tumors. Radiology 140, 767–772
Theman T, Williams WG, Simpson JS, Radford D, Rubin S, Stephens CA (1978) Tumor invasion of the upper inferior vena cava: the use of profound hypothermic and circulatory arrest as a surgical adjunct. J Pediatr Surg 13: 331–334
Utley JR, Mobin-Uddin K, Segnitz RH, Belin RP, Utley JF (1973) Acute obstruction of tricuspid valve by Wilms' tumor. J Thorac Cardiovasc Surg 66: 626–628
Weeks DA, Beckwith JB, Mierau GW, Luckley DW (1989) Rhabdoid tumor of kidney. A report of 111 cases from National Wilms' Tumour Study Pathology Center. Am J Surg Pathol 13: 439–458
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Crankson, S., Ahmed, S., Kumar, N. et al. Rhabdoid tumour of the kidney with caval and cardiac extension. Pediatr Surg Int 7, 225–228 (1992). https://doi.org/10.1007/BF00175849
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DOI: https://doi.org/10.1007/BF00175849