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Surgical repair in a patient with Berry syndrome

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Abstract

Berry syndrome is a trilogy involving an aorto-pulmonary window, right pulmonary artery from ascending aorta and an interrupted aortic arch. Surgical repair for this anomaly is associated with a high mortality rate and incidence of right pulmonary arterial stenosis. Herein, we present the case of a patient with Berry syndrome, who underwent a rapid two-stage repair involving bilateral pulmonary arterial banding and complete repair. Postoperative computed tomography scan showed well-repaired great vessels free of obstruction.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Kanazawa Medical University, 1-1 Daigaku, Uchinadamachi, Kahoku-gun, Ishikawa, 920-0293, Japan

    Makoto Ando, Yuki Ichimori & Shigeru Sakamoto

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  1. Makoto Ando
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  2. Yuki Ichimori
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  3. Shigeru Sakamoto
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Correspondence to Makoto Ando.

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The authors have not received any support from any organization, and thus have no conflicts of interest directly relevant to the content of this article.

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This study was approved by the institutional review board of Kanazawa Medical University, and ethical approval and written informed consent were waived.

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Ando, M., Ichimori, Y. & Sakamoto, S. Surgical repair in a patient with Berry syndrome. Gen Thorac Cardiovasc Surg 68, 1475–1478 (2020). https://doi.org/10.1007/s11748-020-01301-w

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  • DOI: https://doi.org/10.1007/s11748-020-01301-w

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