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Intraosseous malignant peripheral nerve sheath tumor at the frontal bone in a child: a rare cause of proptosis

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Abstract

We report a nine-year-old male having malignant peripheral nerve sheath tumor (MPNST) of the frontal bone, represented with a twelve-month history of ptosis and proptosis in his right eye and enlarged rapidly in the last three months. Except for slight numbness at his one-third of the right forehead, he had no neurological deficit. The patient’s both eyes were having normal eye movements, and he had no visual acuity or field loss. After surgery, we observed the patient with no recurrence for 4 years.

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Acknowledgements

The study was conducted at Akdeniz University Faculty of Medicine.

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Authors and Affiliations

  1. Department of Ophthalmology, Faculty of Medicine, Akdeniz University, Antalya, 07070, Turkey

    Cisil Erkan Pota, Hatice Deniz İlhan, Mehmet Erkan Doğan & Ahmet Burak Bilgin

  2. Department of Neurosurgery, Faculty of Medicine, Akdeniz University, Antalya, Turkey

    Ethem Taner Göksu

  3. Department of Pathology, Faculty of Medicine, Akdeniz University, Antalya, Turkey

    Elif İnanç Gurer

Authors
  1. Cisil Erkan Pota
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  2. Hatice Deniz İlhan
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  3. Mehmet Erkan Doğan
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  4. Ethem Taner Göksu
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  5. Ahmet Burak Bilgin
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  6. Elif İnanç Gurer
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Contributions

Hatice Deniz İlhan, Ethem Taner Göksu, and Elif İnanç Gürer made substantial contributions to the conception and design of the work; Çisil Erkan Pota, Mehmet Erkan Doğan, Ahmet Burak Bilgin made the acquisition, analysis, and interpretation of data; Ahmet Burak Bilgin made the creation of new software used in the work; Çisil Erkan Pota have drafted the work or substantively revised it.

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Correspondence to Hatice Deniz İlhan.

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Pota, C.E., İlhan, H.D., Doğan, M.E. et al. Intraosseous malignant peripheral nerve sheath tumor at the frontal bone in a child: a rare cause of proptosis. Childs Nerv Syst 39, 1941–1944 (2023). https://doi.org/10.1007/s00381-023-05898-0

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