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Malignant Peripheral Nerve Sheath Tumor, a rare Intraosseous Malignancy in the Mandible of a Patient with Neurofibromatosis Type 1: A Case Report

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

Malignant peripheral nerve sheath tumor (MPNST) is a rare malignancy of nervous tissue. The oral incidence of this lesion is extremely low. MPNST can occur sporadically or in association with neurofibromatosis. We report a rare intraosseous MPNST in the mandible of a 33-year-old female patient with neurofibromatosis type 1.

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No funding was received for conducting this study.

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Authors and Affiliations

  1. Department of Oral & Maxillofacial Surgery, School of Dentistry, Hamadan University of Medical Sciences, Hamadan, Iran

    Omid Soltaninia, Faryad Fatehi & Hamid Naderi

  2. Department of Pathology, School of Medicine, Hamadan University of Medical Sciences, Hamadan, Iran

    Arash Dehghan

Authors
  1. Omid Soltaninia
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  2. Arash Dehghan
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  3. Faryad Fatehi
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  4. Hamid Naderi
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Correspondence to Hamid Naderi.

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The authors have no financial or proprietary interests in any material discussed in this article. There was no need for the ethics committee’s approval in presenting this case. Informed consent was obtained from the patient to report the patient’s documents.

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Soltaninia, O., Dehghan, A., Fatehi, F. et al. Malignant Peripheral Nerve Sheath Tumor, a rare Intraosseous Malignancy in the Mandible of a Patient with Neurofibromatosis Type 1: A Case Report. Indian J Otolaryngol Head Neck Surg 75, 3839–3842 (2023). https://doi.org/10.1007/s12070-023-03885-0

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  • DOI: https://doi.org/10.1007/s12070-023-03885-0

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