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Malignant nerve sheath tumor of oculomotor nerve in a pediatric patient

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Abstract

Malignant nerve sheath tumors are extremely rare pathologies. They tend to occur within peripheral nerves and have close association of neurofibromatosis disease. Here, we present the second case of MNST of oculomotor nerve in literature. The patient was a 2-year-old girl with left sided oculomotor nerve palsy. After resection, the patient immediately had chemotherapy and radiotherapy. One year after surgery disease progressed with extensive intracranial seedings, and she passed away.

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Authors and Affiliations

  1. Division of Pediatric Neurosurgery, Department of Neurosurgery, Acıbadem University School of Medicine, Istanbul, Turkey

    Ekin Altınbaş, Bahattin Tanrıkulu & M. Memet Özek

  2. Department of Pathology, Acıbadem University School of Medicine, Istanbul, Turkey

    Ayça Erşen Danyeli

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  1. Ekin Altınbaş
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  2. Bahattin Tanrıkulu
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  3. Ayça Erşen Danyeli
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  4. M. Memet Özek
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Correspondence to Bahattin Tanrıkulu.

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Altınbaş, E., Tanrıkulu, B., Danyeli, A.E. et al. Malignant nerve sheath tumor of oculomotor nerve in a pediatric patient. Childs Nerv Syst 38, 807–811 (2022). https://doi.org/10.1007/s00381-021-05283-9

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  • DOI: https://doi.org/10.1007/s00381-021-05283-9

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