Abstract
Purpose
To provide the reader with a comprehensive but concise understanding of congenital scoliosis
Methods
We have undertaken to summarize available literature on the pathophysiology, epidemiology, and management of congenital scoliosis.
Results
Congenital scoliosis represents 10% of pediatric spine deformity and is a developmental error in segmentation, formation, or a combination of both leading to curvature of the spine. Treatment options are complicated by balancing growth potential with curve severity. Often associated abnormalities of cardiac, genitourinary, or intraspinal systems are concurrent and should be evaluated as part of the diagnostic work-up. Management balances the risk of progression, growth potential, lung development/function, and associated risks. Surgical treatment options involve growth-permitting systems or fusions.
Conclusion
Congenital scoliosis is a complex spinal problem associated with many other anomalous findings. Treatment options are diverse but enable optimization of management and care of these children.
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The authors acknowledge the assistance of Carolyn Hendrix and Brian O’Doherty in the preparation of this article.
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AFS: Consultant: DePuy Synthes Spine, Ethicon, Globus Medical, NuVasive, Stryker, Zimmer Biomet. Royalties: NuVasive, Zimmer Biomet. Executive Committee: Setting Scoliosis Straight Foundation and Children’s Spine Study Group
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SWH: Speakers bureau: NuVasive. Consultant: NuVasive. Consultant: Auctus. Stocks/options: Auctus. Speakers bureau: Zimmer Biomet
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Mackel, C.E., Jada, A., Samdani, A.F. et al. A comprehensive review of the diagnosis and management of congenital scoliosis. Childs Nerv Syst 34, 2155–2171 (2018). https://doi.org/10.1007/s00381-018-3915-6
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DOI: https://doi.org/10.1007/s00381-018-3915-6