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Lymphangiomas and Lymphangiomatosis

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Atlas of Genetic Diagnosis and Counseling

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Abstract

Lymphangiomas are histologically benign but may have life-threatening potential with increasing size and encroachment of adjacent vital structures. Lymphangiomatosis is an extremely rare pathological condition where multiple lymphangiomas are present and may affect the visceral organs (lung, liver, and spleen), soft tissues, subcutaneous tissues, skin, and bones (long bones, pelvis, skull, vertebrae).

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Authors and Affiliations

  1. Medical Genetics, Shriners Hospitals for Children, Perinatal and Clinical Genetics, Department of Pediatrics, LSU Health Sciences Center, Shreveport, LA, USA

    Harold Chen

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  1. Harold Chen
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Chen, H. (2017). Lymphangiomas and Lymphangiomatosis. In: Atlas of Genetic Diagnosis and Counseling. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2401-1_263

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  • DOI: https://doi.org/10.1007/978-1-4939-2401-1_263

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  • Print ISBN: 978-1-4939-2400-4

  • Online ISBN: 978-1-4939-2401-1

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