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Choledochal Cyst

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Rickham's Neonatal Surgery

Abstract

A choledochal cyst (congenital dilatation of the bile duct) shows extra and/or intrahepatic dilatation of the bile duct, and mainly cystic dilatation of the common bile duct. Although the etiology is unknown, it might be congenital. In 1936, Yotsuyanagi suggested a new etiological theory based on unequal epithelial proliferation at the stage of the physiological occlusion of the primitive choledochus. Thereafter, Babbit proposed an abnormal relationship between the common bile duct and pancreatic duct. However, Rustad and Lilly suggested that this abnormal relationship was simply a malformation associated with a choledochal cyst. Therefore, the etiology has not yet been established.

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Authors and Affiliations

  1. Department of Surgery, Meiji University of Integrative Medicine, Kyoto, Japan

    Naomi Iwai MD, PhD

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  1. Naomi Iwai MD, PhD
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Correspondence to Naomi Iwai MD, PhD .

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Editors and Affiliations

  1. Division of Child Health, Alder Hey Children’s NHS Foundation Trust, Liverpool, United Kingdom

    Paul D. Losty

  2. University of Pennsylvania , Philadelphia, Pennsylvania, USA

    Alan W. Flake

  3. Childrens Hospital, University of Helsinki, Helsinki, Finland

    Risto J. Rintala

  4. Royal Children’s Hospital, University of Melbourne, Parkville, Victoria, Australia

    John M. Hutson

  5. Department of Surgery, Meiji University of Integrative Medicine, Kyoto, Japan

    Naomi lwai

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Iwai, N. (2018). Choledochal Cyst. In: Losty, P., Flake, A., Rintala, R., Hutson, J., lwai, N. (eds) Rickham's Neonatal Surgery. Springer, London. https://doi.org/10.1007/978-1-4471-4721-3_43

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  • DOI: https://doi.org/10.1007/978-1-4471-4721-3_43

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