Definition and Characteristics
Amyloidoses are rare disorders characterized by the extracellular deposition of amyloid in various organs leading to organic damage and dysfunction. The skin may be involved as the only organ – localized cutaneous amyloidosis – or in the course of systemic (generalized) amyloidosis. Within these two categories, several clinical variants can be distinguished and on pathogenetic grounds be classified as primary or secondary manifestations, and also be divided into hereditary and nonhereditary forms (see Table 1).
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Emberger, M., Hintner, H., Hawranek, T. (2009). Amyloidoses, Cutaneous. In: Lang, F. (eds) Encyclopedia of Molecular Mechanisms of Disease. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-29676-8_438
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DOI: https://doi.org/10.1007/978-3-540-29676-8_438
Publisher Name: Springer, Berlin, Heidelberg
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