Profiling of T Cell Repertoire in SARS-CoV-2-Infected COVID-19 Patients Between Mild Disease and Pneumonia Che-Mai ChangPo‐Hao FengWei-Chiao Chang Original Article 05 May 2021 Pages: 1131 - 1145
Robust Antibody and T Cell Responses to SARS-CoV-2 in Patients with Antibody Deficiency Hannah KinoshitaJessica Durkee-ShockMichael D. Keller Original Article 13 May 2021 Pages: 1146 - 1153
MHC Haplotyping of SARS-CoV-2 Patients: HLA Subtypes Are Not Associated with the Presence and Severity of COVID-19 in the Israeli Population Shay Ben ShacharNoam BardaYoram Louzoun Original Article 29 May 2021 Pages: 1154 - 1161
Evolution of the Human Cytokine Response from Acute Illness to Disease Resolution in SARS-Cov-2 Infection—Implications for Therapeutic Monitoring and Therapeutic Targets George P. DrewettAna CopaescuJason A. Trubiano Letter to Editor 16 April 2021 Pages: 1162 - 1164
SARS-CoV-2 Infection in a Child with Severe Congenital Neutropenia Pandiarajan VigneshSanjib MondalMan Updesh Singh Sachdeva Letter to Editor 03 May 2021 Pages: 1165 - 1168
Neutralizing Autoantibodies to Type I Interferons in COVID-19 Convalescent Donor Plasma Sara E. VazquezPaul BastardJoseph L. DeRisi Letter to Editor Open access 19 May 2021 Pages: 1169 - 1171
Haploidentical Stem Cell Transplant with Post-Transplant Cyclophosphamide in Pediatric Hemophagocytic Lymphohistiocytosis Diego Medina-ValenciaDaniela ClevesManuela Olaya Original Article 09 March 2021 Pages: 1172 - 1177
Atypical Presentation of Severe Fungal Necrotizing Fasciitis in a Patient with X-Linked Agammaglobulinemia Chai Teng ChearRevathy NallusamyAdiratna Mat Ripen Original Article 13 March 2021 Pages: 1178 - 1186
Rapid Flow Cytometry-Based Assay for the Functional Classification of MEFV Variants Yoshitaka HondaYukako MaedaRyuta Nishikomori Original Article 17 March 2021 Pages: 1187 - 1197
Severe Fatigue Is Common Among Pediatric Patients with Primary Immunodeficiency and Is Not Related to Disease Activity Linde N. NijhofMarco van BrusselSanne L. Nijhof Original Article Open access 17 March 2021 Pages: 1198 - 1207
Humoral Immunodeficiency and Immune Globulin Replacement Therapy (IGRT) Usage in DiGeorge Syndrome Sara H. SoshnickTuhina JosephNicholas J. Bennett Original Article 19 March 2021 Pages: 1208 - 1212
Diagnostic Challenges in Pediatric Hemophagocytic Lymphohistiocytosis Stephanie J. SiSarah K. TasianKathleen E. Sullivan Original Article 24 March 2021 Pages: 1213 - 1218
A Minimal Parameter Set Facilitating Early Decision-making in the Diagnosis of Hemophagocytic Lymphohistiocytosis Bas M. SmitsJoris van MontfransStefan Nierkens Original Article Open access 29 March 2021 Pages: 1219 - 1228
The Innate Immune Response Characterizes Posterior Reversible Encephalopathy Syndrome Christopher NelkeAndreas Schulte-MecklenbeckTobias Ruck Original Article Open access 12 April 2021 Pages: 1229 - 1240
Abnormal SCID Newborn Screening and Spontaneous Recovery Associated with a Novel Haploinsufficiency IKZF1 Mutation Hye Sun KuehnNicholas J. GloudeCathleen Collins Original Article 14 April 2021 Pages: 1241 - 1249
Altered Spectrum of Lymphoid Neoplasms in a Single-Center Cohort of Common Variable Immunodeficiency with Immune Dysregulation Claudia WehrLeonora HouetAnnette Schmitt-Graeff Original Article Open access 19 April 2021 Pages: 1250 - 1265
Current Spectrum of Infections in Patients with X-Linked Agammaglobulinemia Olivier PaccoudNizar Mahlaouithe CEREDIH network Original Article 21 April 2021 Pages: 1266 - 1271
Genomic Spectrum and Phenotypic Heterogeneity of Human IL-21 Receptor Deficiency Deniz CagdasDaniel MayrStuart G. Tangye Original Article 30 April 2021 Pages: 1272 - 1290
Clinical Manifestations, Mutational Analysis, and Immunological Phenotype in Patients with RAG1/2 Mutations: First Cases Series from Mexico and Description of Two Novel Mutations Saul Oswaldo Lugo-ReyesNina PastorMario Ernesto Cruz-Munoz Original Article 05 May 2021 Pages: 1291 - 1302
Clinical Features of Female Taiwanese Carriers with X-linked Chronic Granulomatous Disease from 2004 to 2019 Chao-Yi WuYi-Ching ChenCheng-Hsun Chiu Original Article 08 May 2021 Pages: 1303 - 1314
Decreased ATM Function Causes Delayed DNA Repair and Apoptosis in Common Variable Immunodeficiency Disorders Chantal E. HargreavesSilvia SalatinoSmita Y. Patel Original Article Open access 19 May 2021 Pages: 1315 - 1330
Steady-State Serum IgG Trough Levels Are Adequate for Pharmacokinetic Assessment in Patients with Immunodeficiencies Receiving Subcutaneous Immune Globulin Zhaoyang LiBarbara McCoyLeman Yel Original Article Open access 26 May 2021 Pages: 1331 - 1338
Consensus Middle East and North Africa Registry on Inborn Errors of Immunity Asghar AghamohammadiNima RezaeiHassan Abolhassani Original Article Open access 29 May 2021 Pages: 1339 - 1351
A Case of Severe Combined Immunodeficiency Missed by Newborn Screening Maleewan KitcharoensakkulJahnavi AluriJeffrey J. Bednarski Letter to Editor 12 March 2021 Pages: 1352 - 1355
A New Missense Mutation in CD79B Leads to Autosomal Recessive Agammaglobulinemia in Two Siblings Steve GenebrierMathieu FusaroCapucine Picard Letter to Editor 17 March 2021 Pages: 1356 - 1360
Autosomal Recessive ISG15 Deficiency Underlies Type I Interferonopathy with Systemic Lupus Erythematosus and Inflammatory Myositis Sulaiman M. Al-MayoufLujayn AkbarHamoud Al-Mousa Letter to Editor 19 March 2021 Pages: 1361 - 1364
Ledipasvir/Sofosbuvir Eradicates Hepatitis C in an Immunodeficient STAT3-GOF Patient Julian ThalhammerMaria Elena MaccariCarsten Speckmann Letter to Editor Open access 29 March 2021 Pages: 1365 - 1367
Anakinra for Treatment of Liver Abscesses in a Patient with a Novel CYBB Variant of Chronic Granulomatous Disease Caroline ToAndrew WilliamsLuke Droney Letter to Editor 06 April 2021 Pages: 1368 - 1371
Epstein-Barr Virus–Negative Granulomatous Disease Due to SAP Deficiency Takao KarasawaKo KudoKiminori Terui Letter to Editor 07 April 2021 Pages: 1372 - 1375
A Novel TRAF3IP2 Mutation Causing Chronic Mucocutaneous Candidiasis Filipa MarujoSimon J. PelhamJoão Farela Neves Letter to Editor 07 April 2021 Pages: 1376 - 1379
Dramatic Efficacy of Ibrutinib in a Schnitzler Syndrome Case with Indolent Lymphoma Fabien ClavesRomane SiestSylvain Carras Letter to Editor 19 April 2021 Pages: 1380 - 1383
The Seven STAT3-Related Hyper-IgE Syndromes Ilham FadilMeriem Ben-AliAhmed Aziz Bousfiha Letter to Editor 26 April 2021 Pages: 1384 - 1389
Correction to: The Seven STAT3‑Related Hyper‑IgE Syndromes Ilham FadilMeriem Ben‑AliAhmed Aziz Bousfiha Publisher Correction 10 May 2021 Pages: 1390 - 1390
TCF3 Dominant Negative Variant Causes an Early Block in B-Lymphopoiesis and Agammaglobulinemia Ebtehal Al SheikhPeter D. ArkwrightTracy A. Briggs Letter to Editor 27 April 2021 Pages: 1391 - 1394
Skewed TCR Alpha, but not Beta, Gene Rearrangements and Lymphoma Associated with a Pathogenic TRAC Variant Amit RawatAnkita SinghSurjit Singh Letter to Editor 28 April 2021 Pages: 1395 - 1399
DOCK2 Deficiency Diagnosed 18 Years After Hematopoietic Stem Cell Transplantation Katherine D’Astous-GauthierAléhandra DesjardinsHugo Chapdelaine Letter to Editor 30 April 2021 Pages: 1400 - 1402
Hematopoietic Stem Cell Transplantation Cures Chronic Aichi Virus Infection in a Patient with X-linked Agammaglobulinemia Giorgia BucciolThomas TousseynIsabelle Meyts Letter to Editor 04 May 2021 Pages: 1403 - 1405
Inflammatory Bowel Disease and Guillain Barre Syndrome in FCHO1 Deficiency Sezin AydemirAli IslekAhmet Ozen Letter to Editor 05 May 2021 Pages: 1406 - 1410
A Family with a Novel CTLA4 Haploinsufficiency Mutation and Neurological Symptoms Alexandros GrammatikosSarah JohnstonMark Gompels Letter to Editor Open access 06 May 2021 Pages: 1411 - 1416
Disseminated Tuberculosis in a Patient with Autosomal Recessive p47phox Chronic Granulomatous Disease Ximena León-LaraAlejandro Campos-MurguíaLizbeth Blancas-Galicia Letter to Editor 19 May 2021 Pages: 1417 - 1419
Complicated Diagnosis and Treatment of HA20 due to Contiguous Gene Deletions involving 6q23.3 Chung Wah WuGhadir SasaBo Yuan Letter to Editor 25 May 2021 Pages: 1420 - 1423