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Desmoid-type fibromatosis arising in a bifid rib chest wall

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General Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Desmoid-type fibromatosis is a rare soft tissue tumor and the chest wall is one of the common sites of its extra-abdominal occurrence. A bifid rib is one of the congenital rib abnormalities. We report a case of desmoid-type fibromatosis arising in a chest wall’s bifid rib. A 42-year-old female complained of right chest pain without remarkable medical, traumatic, or familial history. Chest-computed tomography revealed a chest wall tumor located adjacent to a bifid costal cartilage of third rib. We performed chest wall resection of second and third ribs. Pathologically, the tumor was diagnosed a desmoid-type fibromatosis of the chest wall. We surmise mechanical stimulation due to the bifid rib may be related to the occurrence of the tumor. In case of desmoid-type fibromatosis without somatic gene mutation, traumatic history, wound, implants, or use of female hormonal agents, we should search also local congenital abnormality.

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Authors and Affiliations

  1. Division of Thoracic Surgery, Department of Surgery, The Jikei University School of Medicine, 3-25-8 Nishishinbashi, Minatoku, Tokyo, 105-0003, Japan

    Shohei Mori, Yuki Noda, Daiki Kato & Takashi Ohtsuka

  2. Department of Pathology, The Jikei University School of Medicine, Tokyo, Japan

    Shinichi Hirooka

Authors
  1. Shohei Mori
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  2. Yuki Noda
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  3. Daiki Kato
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  4. Shinichi Hirooka
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  5. Takashi Ohtsuka
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Correspondence to Shohei Mori.

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Mori, S., Noda, Y., Kato, D. et al. Desmoid-type fibromatosis arising in a bifid rib chest wall. Gen Thorac Cardiovasc Surg 67, 996–998 (2019). https://doi.org/10.1007/s11748-019-01088-5

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  • DOI: https://doi.org/10.1007/s11748-019-01088-5

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