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Cutaneous lesions in occult spinal dysraphism—correlation with intraspinal findings

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Abstract

Objects

This study was conducted to investigate the frequency and type of cutaneous stigmata in different forms of occult spinal dysraphism (OSD) and their correlation to the underlying malformation.

Methods

Fourteen different forms of spinal malformations were identified in 358 operated patients with OSD. Most frequent findings (isolated or in combinations) were spinal lipoma, split cord malformation, pathologic filum terminale, dermal sinus, meningocele manqué, myelocystocele and caudal regression. Stigmata were present in 86.3% of patients, often in various combinations. Using a binary logistic regression analysis, significant correlations with distinct malformations were found for subcutaneous lipomas, skin tags, vascular nevi, pori, hairy patches, hypertrichosis, meningoceles and “cigarette burn” marks.

Conclusions

Cutaneous markers in a high percentage accompany spinal malformations. Due to the correlations of different stigmata to distinct malformations, they can aid the clinician in further diagnostic and therapeutic work.

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Authors and Affiliations

  1. University Children’s Hospital Wuerzburg, Josef-Schneider-Strasse 2, 97080, Würzburg, Germany

    C. Schropp

  2. Department of Pediatric Neurosurgery, University of Würzburg, Würzburg, Germany

    N. Sörensen, H. Collmann & J. Krauß

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  1. C. Schropp
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  2. N. Sörensen
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  3. H. Collmann
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  4. J. Krauß
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Correspondence to C. Schropp.

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Schropp, C., Sörensen, N., Collmann, H. et al. Cutaneous lesions in occult spinal dysraphism—correlation with intraspinal findings. Childs Nerv Syst 22, 125–131 (2006). https://doi.org/10.1007/s00381-005-1150-4

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  • DOI: https://doi.org/10.1007/s00381-005-1150-4

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