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Bilateral acoustic neurofibromatosis camouflaged by corticosteroid treatment of sudden sensorineural hearing loss

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Abstract

We report a case of bilateral acoustic neurofibromatosis which presented with the atypical symptom of sudden sensorineural deafness. Following corticosteroid therapy the hearing loss returned to near normal levels. The pathogenesis of reversible sudden sensorineural hearing loss in the presence of an acoustic neuroma is discussed. The importance of Gadolinium-enhanced magnetic resonance imaging in the detection of bilateral acoustic neurofibromatosis is highlighted by the case report.

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References

  1. Martuza, R. L., Eldridge, R. Neurofibromatosis 2 (bilateral acoustic neurofibromatosis N). Eng. J. Med. 1988; 318: 684.

    CAS  Google Scholar 

  2. Royleau, G. A., Wertelecki, W., Haines, J. L. Genetic linkage of bilateral acoustic neurofibromatosis to a DNA marker on chromosome 22. Nature 1987: 329: 246–248.

    Article  Google Scholar 

  3. Linthicum, F. J. Jr. Unusual audiometric and histologic findings in bilateral acoustic neuromas. Annals Otol. Rhinol. Laryngol. 1972: 81: 433–437.

    Google Scholar 

  4. Linthicum, F. H., Khalessi, M. H., Churchill, D. In Acoustic tumours (House, W. F. and Leutze, C. M., eds.). 1979: vol. 1: 237. University Park Press, Baltimore.

    Google Scholar 

  5. Eckermeier, L., Pirsig, W., Mueller, D. Histopathology of 30 nonoperated acoustic schwannomas. Arch. Otolaryngology 1979: 222: 1–9.

    CAS  Google Scholar 

  6. Linthicum, F. H., Brackmann, D. E. Bilateral acoustic tumors. A diagnostic and surgical challenge. Arch. Otolaryngology 1980: 106: 729–733.

    Google Scholar 

  7. Higgs, M. L. Sudden deafness as the presenting symptom of acoustic neuroma. Arch. Otolaryngology 1973: 98: 73–6.

    CAS  Google Scholar 

  8. Pensak, M. L., Gasscock, M. E. III., Josey, A. F., Jackson, C. G., Gulya, A. J. Sudden hearing loss and cerebellopontine angle tumors. Laryngoscope 1985: 95: 1188–93.

    Article  PubMed  CAS  Google Scholar 

  9. Berg, H. M., Cohen, N. L., Hammerschlag, P. E., Waltzman, S. B. Acoustic neuroma presenting as sudden hearing loss with recovery. Otolaryngology Head and Neck surgery 1986: 94: 15–22.

    PubMed  CAS  Google Scholar 

  10. Mattox, O. E., Simmons, F. B. Natural history of sudden sensorineural hearing loss. Annals Otol. Rhinol. Laryngol. 1977: 86: 463–80.

    CAS  Google Scholar 

  11. Noskowitz, D., Lee, K. J., Smith, H. W. Steroid use in idiopathic sudden sensorineural hearing loss. Laryngoscope 1984: 94: 664–6.

    Google Scholar 

  12. Nedzelski, J. M., Dufour, J. J. Acoustic neuroma presenting as sudden deafness. Journal of Otorhinolaryngology and Related Specialities 1975: 37: 271–9.

    CAS  Google Scholar 

  13. Cohen, N. L. Acoustic neuroma surgery with emphasis on preservation of hearing. Laryngoscope 1979: 89: 886–96.

    Article  PubMed  CAS  Google Scholar 

  14. Chow, J. M., Garcia, J. Acoustic neuroma presenting as sudden hearing loss. American Journal of Otolaryngoloy 1985: 6: 115–9.

    Article  CAS  Google Scholar 

  15. Berenholz, L. P., Eriksen, C., Hirsh, F. A. Recovery from repeated sudden hearing loss with corticosteroid use in the presence of an acoustic neuroma. Annals Otol. Rhinol. Laryngol. 1992: 101: 827–831.

    CAS  Google Scholar 

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Authors and Affiliations

  1. Department of Otorhinolaryngology Head and Neck Surgery, Royal College of Surgeons in Ireland and Beaumont Hospital, Dublin

    R. J. Gaffney

  2. Department of Otolaryngology, Adelaide Hospital, Dublin

    D. P. McShane

Authors
  1. R. J. Gaffney
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  2. D. P. McShane
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Gaffney, R.J., McShane, D.P. Bilateral acoustic neurofibromatosis camouflaged by corticosteroid treatment of sudden sensorineural hearing loss. I.J.M.S. 165, 151–152 (1996). https://doi.org/10.1007/BF02940237

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  • DOI: https://doi.org/10.1007/BF02940237

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