Summary
A case of familial benign chronic pemphigus (FBCP Hailey-Hailey disease) in an adult is presented. The areas of predilection are the axillary region and the genito-crural area in addition to the submammary folds. There is no satisfactory medical therapy for this condition. Surgical excision of the affected skin areas with subsequent split-thickness skin grafting has been reported several times in the past. This can give relief of local symptoms. In the present case topical and systemic application of antibiotics, antimycotics and cortisone failed. Therefore a reduction mammoplasty was performed with resection of the involved skin areas. One year after surgery the patient is asymptomatic.
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Balogh, B., Freilinger, G. Familial benign chronic pemphigus Hailey-Hailey —Surgical therapy by excision with simultaneous reduction mammoplasty. Eur J Plast Surg 9, 108–111 (1986). https://doi.org/10.1007/BF00298950
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DOI: https://doi.org/10.1007/BF00298950