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Liver Transplantation for Budd–Chiari Syndrome

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Budd-Chiari Syndrome

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Abstract

Liver transplantation is indicated for rapidly progressing Budd–Chiari syndrome (BCS) after failure of conventional treatment. Outflow reconstruction is key in BCS cases. The area of the venous outflow obstruction varies among cases. The hepatic veins of the liver graft must be anastomosed with a patent outflow tract of the recipient. After transplantation, the 5-year survival rate of patients with BCS is approximately 75%. As patients with BCS are often in a prothrombotic state, long-term anticoagulation therapy should be maintained after liver transplantation.

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Abbreviations

BCS:

Budd–Chiari syndrome

TIPS:

Transjugular intrahepatic portosystemic shunt

HV:

Hepatic veins

IVC:

Inferior vena cava

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Author information

Authors and Affiliations

  1. Department of Transplantation/Pediatric Surgery, Postgraduate School of Life Science, Kumamoto University, Kumamoto, Japan

    Yasuhiko Sugawara & Taizo Hibi

Authors
  1. Yasuhiko Sugawara
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  2. Taizo Hibi
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Corresponding author

Correspondence to Yasuhiko Sugawara .

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Editors and Affiliations

  1. Department of Gastroenterology, General Hospital of Northern Theater Command, Shenyang, Liaoning, China

    Xingshun Qi

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Sugawara, Y., Hibi, T. (2020). Liver Transplantation for Budd–Chiari Syndrome. In: Qi, X. (eds) Budd-Chiari Syndrome. Springer, Singapore. https://doi.org/10.1007/978-981-32-9232-1_14

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  • DOI: https://doi.org/10.1007/978-981-32-9232-1_14

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-32-9231-4

  • Online ISBN: 978-981-32-9232-1

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