Malignant Solitary Fibrous Tumor, Pleural

Synonyms

Although malignant solitary fibrous tumor has been reported under a variety of different names, these names are not preferred.

Definition

Malignant solitary fibrous tumor of the pleura is the malignant counterpart of benign solitary fibrous tumor. Like benign solitary fibrous tumor, malignant solitary fibrous tumor is a spindle cell neoplasm considered to arise from submesothelial mesenchymal cells.

Clinical Features

• Incidence

  Solitary fibrous tumors are uncommon pleural tumors, and malignant solitary fibrous tumor of the pleura make up approximately 20–30% of pleural solitary fibrous tumors.

• Age

  Malignant solitary fibrous tumor of the pleura is generally found in adults and is rare in patients under 10 years of age.

• Sex

  Malignant solitary fibrous tumor of the pleura has no gender predilection.

• Site

  Malignant solitary fibrous tumor of the pleura is often attached to the mediastinum or parietal pleura; however, tumors may also arise from the visceral pleura.

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