Abstract
Myopericytoma is a rare type of soft tissue tumor with perivascular myoid differentiation. Although the pathology characteristics of myopericytomas are well described in literature, the clinical characteristics of these tumors have received less attention. We report on a 44-year-old female who developed a myopericytoma in her right distal forearm. The patient presented with a painless solid mass that had been slowly increasing in size for approximately 5 years. Unlike typical myopericytoma in the extremity growing as a subcutaneous nodule, the tumor enveloped the distal ulna. This case suggests a different growth pattern for myopericytoma. Myopericytoma is a rare soft tissue tumor originating from perivascular myoid cells, which has only been recognized as a distinct condition in the past 15 years (Granter et al. Am J Surg Pathol. 22 (5):513-25, 1998). Most of these tumors present as a painless, slow-growing subcutaneous nodule. They have typically been described by pathologists who concentrate on the pathological features rather than the clinical characteristics of these tumors (Granter et al. Am J Surg Pathol. 22 (5):513-25, 1998; Dray et al. J Clin Pathol. 59 (1):67-73, 2006; Mentzel et al. Am J Surg Pathol. 30 (1):104-113 2006). We report a case of myopericytoma with an unusual growth pattern involving the distal forearm to highlight the clinicopathologic features of this tumor.
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Conflict of interest
Guang Yang does not have a conflict of interest.
Evan P. McGlinn does not have a conflict of interest.
Kevin C. Chung does not have a conflict of interest.
Financial Disclosure
Kevin C. Chung declares that the research reported in this publication was supported by the National Institute of Arthritis and Musculoskeletal and Skin Diseases of the National Institutes of Health under Award Number K24 AR053120. The content is solely the responsibility of the authors and does not necessarily represent the official views of the National Institutes of Health.
Guang Yang has no financial disclosure.
Evan P. McGlinn has no financial disclosure.
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All the authors declare that all procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1975, as revised in 2008 (5).
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Informed consent was obtained from all patients for being included in the study. All the authors declare that this manuscript contains no identifying information.
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Yang, G., McGlinn, E.P. & Chung, K.C. Myopericytoma of the distal forearm: a case report. HAND 10, 338–341 (2015). https://doi.org/10.1007/s11552-014-9647-5
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DOI: https://doi.org/10.1007/s11552-014-9647-5