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Absent Aortic and Dysplastic Pulmonary Valves Associated with Ventricular Septal Defect in Fetal Hydrops

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Abstract

We describe worsening cardiac failure in a hydropic male fetus with a large ventricular septal defect associated with severe pulmonary and mild aortic regurgitation detected prenatally by echocardiography. The hemodynamic transition after emergency cesarean section at 31 weeks of gestation resulted in amelioration of the pulmonary incompetence but exacerbation of aortic insufficiency causing coronary steal. Death followed withdrawal of support 4 hours after delivery. Autopsy revealed absent aortic valve cusps, dysplastic pulmonary valve, and a large ventricular septal defect.

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Authors and Affiliations

  1. The Hospital for Children and Adolescents, Division of Pediatric Cardiology and HUCH, Laboratory Diagnostics , Division of Pathology, University Hospital of Helsinki, Finland

    M. Eronen & P. Heikkilä

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  1. M. Eronen
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  2. P. Heikkilä
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Eronen, M., Heikkilä, P. Absent Aortic and Dysplastic Pulmonary Valves Associated with Ventricular Septal Defect in Fetal Hydrops . Pediatr Cardiol 24, 400–402 (2003). https://doi.org/10.1007/s00246-002-0336-8

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  • DOI: https://doi.org/10.1007/s00246-002-0336-8

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