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Duchenne’s Muscular Dystrophy and Spinal Muscular Atrophy

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Non-Idiopathic Spine Deformities in Young Children

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Abstract

Basic features of spinal deformities in Duchenne’s muscular dystrophy and spinal muscular atrophy are described. Guidelines for decision-making are presented. Early posterior instrumentation and fusion is recommended for most cases. The importance of team approach and critical preoperative workup is stressed to avoid complications in these high-risk procedures. Technical points of spine surgery in these conditions are highlighted.

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Authors and Affiliations

  1. ORTON Orthopaedic Hospital, Invalid Foundation, Tenholantie 10, FIN-00280, Helsinki, Finland

    Dietrich Schlenzka

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  1. Dietrich Schlenzka
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Correspondence to Dietrich Schlenzka .

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Editors and Affiliations

  1. Dept. Orthopedics & Traumatology, Hacettepe University, Sihhiye, Ankara, 06100, Turkey

    Muharrem Yazici

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Schlenzka, D. (2011). Duchenne’s Muscular Dystrophy and Spinal Muscular Atrophy. In: Yazici, M. (eds) Non-Idiopathic Spine Deformities in Young Children. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-19417-7_7

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  • DOI: https://doi.org/10.1007/978-3-642-19417-7_7

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-19416-0

  • Online ISBN: 978-3-642-19417-7

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