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Venous-lymphatic Malformations (Lymphangioma) of the Orbit: Diagnostic and Therapeutic Challenges

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Oculoplastics and Orbit

Part of the book series: Essentials in Ophthalmology ((ESSENTIALS))

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Abstract

Vascular anomalies of the orbit include venouslymphatic malformations (VLM). These lesions, often referred to as lymphangioma, are considered congenital and most commonly present in childhood. Approximately one-third are identified in the first weeks of life [17]. VLM represented 4% of 1,264 orbital tumors in Shields’ series [35] and 3% of 600 in Iliff and Green’s series [20]. The most common presenting sign is painful unilateral proptosis resulting from spontaneous hemorrhage (Fig. 7.1a). Less commonly, VLM may enlarge slowly (Fig. 7.2a, b).

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Rudolf Guthoff James Katowitz

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(2007). Venous-lymphatic Malformations (Lymphangioma) of the Orbit: Diagnostic and Therapeutic Challenges. In: Guthoff, R., Katowitz, J. (eds) Oculoplastics and Orbit. Essentials in Ophthalmology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-33677-8_7

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  • DOI: https://doi.org/10.1007/978-3-540-33677-8_7

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-33675-4

  • Online ISBN: 978-3-540-33677-8

  • eBook Packages: MedicineMedicine (R0)

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