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Syndromes de prédisposition héréditaires aux tumeurs endocrines gastro-entéro-pancréatiques

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Tumeurs endocrines thoraciques et digestives

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Abstrait

Des tumeurs endocrines gastro-entéro-pancréatiques (TE GEP) peuvent être observées dans plusieurs syndromes de prédisposition héréditaire: il s’agit essentiellement de la néoplasie endocrinienne multiple de type 1 et de la maladie de von Hippel-Lindau, beaucoup plus rarement de la neurofibromatose de type 1 ou de la sclérose tubéreuse de Bourneville. Ces quatre syndromes ont en commun un mode de transmission autosomique dominant et une pénétrance élevée (16, 26).

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  1. Clinique Marc Linquette, CHRU de Lille, Rue du Pr. Laguesse, 59037, Lille Cedex

    C. Cardot-Bauters

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  1. C. Cardot-Bauters
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© 2008 Springer-Verlag France, Paris

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Cardot-Bauters, C. (2008). Syndromes de prédisposition héréditaires aux tumeurs endocrines gastro-entéro-pancréatiques. In: Tumeurs endocrines thoraciques et digestives. Springer, Paris. https://doi.org/10.1007/978-2-287-35574-5_11

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  • DOI: https://doi.org/10.1007/978-2-287-35574-5_11

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-287-35573-8

  • Online ISBN: 978-2-287-35574-5

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